DOI: 10.1055/s-00000075

Seminars in Respiratory and Critical Care Medicine

Issue 02 · Volume 41 · April 2020 DOI: 10.1055/s-010-46452 Orphan Lung Diseases Guest Editors: Jay H. Ryu, MD, Nishant Gupta, MD

Preface

175
Gupta, Nishant; Ryu, Jay H.: Controversies and Evolving Concepts in Orphan Lung Diseases

Review Article

177
Bolaki, Maria; Antoniou, Katerina M.: Combined Pulmonary Fibrosis and Emphysema
184
Teoh, Alan K. Y.; Corte, Tamera J.: Nonspecific Interstitial Pneumonia
202
Moura, Marta Casal; Gripaldo, Ria; Baqir, Misbah; Ryu, Jay H.: Thoracic Involvement in IgG4-Related Disease
214
Fernández Pérez, Evans R.; Koelsch, Tilman L.; Leone, Paolo M.; Groshong, Steve D.; Lynch, David A.; Brown, Kevin K.: Clinical Decision-Making in Hypersensitivity Pneumonitis: Diagnosis and Management
229
Kropski, Jonathan A.: Familial Interstitial Lung Disease
238
De Jesus Rojas, Wilfredo; Young, Lisa R.: Hermansky–Pudlak Syndrome
247
Kennedy, John C.; Khabibullin, Damir; Boku, Yoseph; Shi, Wei; Henske, Elizabeth P.: New Developments in the Pathogenesis of Pulmonary Cysts in Birt–Hogg–Dubé Syndrome
256
Xu, Kai-Feng; Xu, Wenshuai; Liu, Song; Yu, Jane; Tian, Xinlun; Yang, Yanli; Wang, Shao-Ting; Zhang, Weihong; Feng, Ruie; Zhang, Tengyue: Lymphangioleiomyomatosis
269
Shaw, Brian; Borchers, Michael; Zander, Dani; Gupta, Nishant: Pulmonary Langerhans Cell Histiocytosis
280
Shaw, Brian M.; Shaw, Steven D.; McCormack, Francis X.: Pulmonary Alveolar Microlithiasis
288
Kelly, Alan; McCarthy, Cormac: Pulmonary Alveolar Proteinosis Syndrome
299
Baqir, Misbah; Roden, Anja C.; Moua, Teng: Amyloid in the Lung
311
Ravaglia, Claudia; Poletti, Venerino: Bronchiolitis and Bronchiolar Disorders