Large Supraumbilical Pseudocystic Tumour due to Ectopic Pancreatic Tissue Located in a Rest of the Omphaloenteric Duct

Abstract

Ectopic umbilical pancreatic tissue is extremely rare. We report on a case of a two-year-old boy who suffered from a large recurrent supraumbilical tumour with central cystic degeneration. Ectopic pancreatic tissue was located within the submucosal layer of an umbilical rest of the omphaloenteric duct. Peptic erosion and inflammatory alteration of tissue surrounding the umbilical vein caused recurrent bleeding and formation of a pseudocyst as well as chronical inflammatory granulations within the abdominal wall.

Résumé

Le tissu ombilical pancréatique ectopique est extrêmement rare. Nous faisons un rapport sur un cas d'un garçon de deux ans qui souffrait d'une grosse tumeur supra-ombilicale récurrente kystique. Le tissu pancréatique ectopique était placé dans la sous-muqueuse d'un reste ombilical du conduit omphalo-entérique formant une tumeur pseudo-kystique avec un saignement récurrent secondaire à l'érosion de la veine ombilicale et à l'inflammation.

Resumen

El tejido pancreático umbilical ectópico es extremadamente raro. Presentamos el caso de un niño de 2 años con un gran tumor recurrente supraumbilical con degeneración quística central. El tejido pancreático ectópico estaba localizado en la submucosa de un resto umbilical del conducto onfaloénterico. La erosión péptica e inflamatoria del tejido que rodeaba la vena umbilical causó hemorragia recidivante y pseuodoquiste con inflamación crónica de la pared abdominal.

Zusammenfassung

Umbilikal gelegenes ektopes Pankreasgewebe ist äußerst selten. Wir berichten über einen Fall einer umbilikalen Ektopie von Pankreasgewebe bei einem 2 Jahre alten Jungen mit einem rezidivierenden großen supraumbilikalen Tumor mit zentraler zystischer Degeneration. Das ektope Pankreasgewebe war in der Submukosa eines Restes des Ductus omphaloentericus am Nabel lokalisiert. Offensichtlich aufgrund einer peptischen Erosion und entzündlicher Reaktionen der Umgebung der V. umbilicalis kam es zu rezidivierenden Blutungen mit Bildung einer Pseudozyste und chronisch entzündlicher Granulationen in der umgebenden Bauchwand.

Key words

Ectopic pancreatic tissue - supraumbilical pseudocystic tumour - umbilical vein

Mots-clés

Tissu ectopique pancréatique - tumeur pseudo-cystique supra-ombilicale - veine ombilicale

Palabras clave

Heterotopia pancreática - ombligo - supraumbilical - vena umbilical

Schlüsselwörter

Ektopes Pankreasgewebe - supraumbilikaler pseudozystischer Tumor - Vena umbilicalis

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