Pulmonary Interstitial Emphysema Presenting as a Congenital Cystic Adenomatous Malformation on CT

Introduction

The clinical signs and symptoms of a patient with respiratory distress are usually insufficient to make a diagnosis of the underlying pathology without radiographic assistance. Computed tomography has been increasingly relied on for the accurate diagnosis of congenital cystic adenoid malformation (CCAM). We report here on our experience in a patient with the radiographic appearance of CCAM who, in fact, had pulmonary interstitial emphysema (PIE).

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