The French Experience with a Population-Based Esophageal Atresia Registry (RENATO)

Rony Sfeir; Madeleine Aumar; Dyuti Sharma; Julien Labreuche; Luc Dauchet; Frederic Gottrand

doi:10.1055/a-2206-6837

European Journal of Pediatric Surgery, Table of Contents

Eur J Pediatr Surg 2024; 34(02): 137-142
DOI: 10.1055/a-2206-6837

Review Article

The French Experience with a Population-Based Esophageal Atresia Registry (RENATO)

Rony Sfeir

¹Division of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Reference Center for Congenital and Malformative Esophageal Disorders, Jeanne de Flandre Children's Hospital, Lille University Faculty of Medicine, Lille Cedex, Lille, France

,

Madeleine Aumar

¹Division of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Reference Center for Congenital and Malformative Esophageal Disorders, Jeanne de Flandre Children's Hospital, Lille University Faculty of Medicine, Lille Cedex, Lille, France

,

Dyuti Sharma

¹Division of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Reference Center for Congenital and Malformative Esophageal Disorders, Jeanne de Flandre Children's Hospital, Lille University Faculty of Medicine, Lille Cedex, Lille, France

,

Julien Labreuche

²SEED: Statistique, Evaluation, Economique, Data-Management Maison Régionale de la Recherche Clinique University Hospital of Lille, France - Health Statistics, Lille, France

,

Luc Dauchet

³Department of Epidemiology and Public Health, University Hospital of Lille, France - Public Health, Lille, France

,

Frederic Gottrand

¹Division of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Reference Center for Congenital and Malformative Esophageal Disorders, Jeanne de Flandre Children's Hospital, Lille University Faculty of Medicine, Lille Cedex, Lille, France

› Author Affiliations

Abstract

This paper presented a national register for esophageal atresia (EA) started in January 2008. We report our experience about the conception of this database and its coordination. Data management and data quality are also detailed. In 2023, more than 2,500 patients with EA are included. Prevalence of EA in France was calculated at 1.8/10,000 live birth. Main clinical results are listed with scientific publications issued directly from the register.

Keywords

population-based register - esophageal atresia - rare disease

Full Text

References

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