Ressecção do tumor e colocação de enxerto de pele parcial no couro cabeludo em um paciente com neurofibromatose tipo 1

▪ RESUMO

A neurofibromatose tipo 1 (NF1) é um distúrbio neurocutâneo hereditário no qual se formam tumores no sistema nervoso (neurofibromas). Os neurofibromas são os tumores benignos mais comuns na NF1. O tipo, o tamanho, o número e a localização dos neurofibromas devem ser considerados para a escolha do tratamento. Apresentamos um caso de NF1, no qual foi realizada uma ampla ressecção do couro cabeludo devido à presença de múltiplos neurofibromas. Associado a isso, a reconstrução foi realizada com retalhos de avanço mais autoenxerto de pele parcial, com resultados favoráveis e boa cobertura das áreas onde os tumores foram removidos.

Descritores:

Transplante autólogo - Neurofibromatose 1 - Neurofibroma - Couro cabeludo - Procedimentos de cirurgia plástica

Instituição: Departamento de Cirugía Plástica Reconstructiva, Hospital Nacional Eduardo Rebagliati Martins, Lima, Peru.

Publication History

Received: 07 June 2023

Accepted: 04 February 2024

Article published online:
20 May 2025

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