Eur J Pediatr Surg 2008; 18(2): 117-118
DOI: 10.1055/s-2007-989376
Case Report

© Georg Thieme Verlag KG Stuttgart · New York

Respiratory Distress Secondary to Nasopharyngeal Glial Heterotopia

N. Pakkasjärvi1 , P. Salminen1 , T. Kalajoki-Helmiö2 , R. Rintala1 , A. Pitkäranta3
  • 1Department of Pediatric Surgery, Hospital for Children and Adolescents, University of Helsinki, Helsinki, Finland
  • 2Department of Radiology, Helsinki University Central Hospital, Helsinki Medical Imaging Center, Helsinki, Finland
  • 3Department of Otorhinolaryngology and Head & Neck Surgery, University of Helsinki, Helsinki, Finland
Further Information

Publication History

received Sept 17, 2007

accepted after revision October 9, 2007

Publication Date:
25 April 2008 (online)

Abstract

Nasal glial heterotopia (nasal glioma) is a rare congenital malformation of neural origin. We present a newborn baby with life-threatening respiratory distress secondary to nasopharyngeal glial heterotopia that obstructed the nasopharyngeal or nasal airway. A high degree of suspicion, early diagnosis and surgical management are essential to cure this rare and potentially life-threatening disorder.

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Dr. MD/PhD Niklas Pakkasjärvi

Department of Pediatric Surgery
Hospital for Children and Adolescents

Stenbäckinkatu 11, PO Box 281

00029 HUS, Helsinki

Finland

Email: niklas.pakkasjarvi@helsinki.fi

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