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CC BY 4.0 · Revista Brasileira de Cirurgia Plástica (RBCP) – Brazilian Journal of Plastic Surgery 2025; 40: s00451807279
DOI: 10.1055/s-0045-1807279
Relato de Caso

Dermatofibrosarcoma Protuberans of the Scalp: Case Report

Artikel in mehreren Sprachen: português | English
Jefferson Lessa Soares de Macedo 
1   Hospital Regional da Asa Norte, Unidade de Cirurgia Plástica, Brasília, DF, Brasil
,
Jovita Maria Rafael Batista de Albuquerque Espíndola 
1   Hospital Regional da Asa Norte, Unidade de Cirurgia Plástica, Brasília, DF, Brasil
,
Thamara de Oliveira Vasconcelos 
1   Hospital Regional da Asa Norte, Unidade de Cirurgia Plástica, Brasília, DF, Brasil
,
Luna D'Angelis Barbosa de Albuquerque 
1   Hospital Regional da Asa Norte, Unidade de Cirurgia Plástica, Brasília, DF, Brasil
,
Sarah Pereira Lima Xavier da Silva 
1   Hospital Regional da Asa Norte, Unidade de Cirurgia Plástica, Brasília, DF, Brasil
,
Luis Felipe Rosa de Macedo 
2   Universidade Católica de Brasília, Curso de Graduação em Medicina, Brasília, DF, Brasil
,
Cecilia Rosa de Macedo 
3   Centro Universitário de Brasília (UniCEUB), Curso de Graduação em Medicina, Brasília, DF, Brasil
,
Simone Correa Rosa 
1   Hospital Regional da Asa Norte, Unidade de Cirurgia Plástica, Brasília, DF, Brasil
› Institutsangaben Financial Support The authors declare that they did not receive financial support from agencies in the public, private, or non-profit sectors to conduct the present study.

Ensaios Clínicos Não. | Clinical Trials None.
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Abstract

Dermatofibrosarcoma protuberans is a rare cutaneous tumor of low malignant grade, with slow, infiltrative growth and a strong tendency towards local recurrence after surgical excision. The most frequently affected anatomic site is the thorax (65%), and the tumor rarely affects the scalp (5%). Its high recurrence rate correlates with poor surgical management, as lesions may be confused with dermatofibroma or keloid. We herein report a case of scalp dermatofibrosarcoma protuberans posing particular challenges due to the proximity to the periosteum, calvaria, dura mater, and brain; the resulting defects often require extensive reconstructive procedures. This case confirms the importance of the accurate diagnosis of the primary lesion and the need for aggressive surgical treatment (excision of 2–3 cm of the lateral margins) to lower the incidence of local relapse.

Keywords

dermatofibrosarcoma - head and neck neoplasms - scalp - surgery - plastic surgery - tissue expansion devices

Authors' Contributions

JLSM: data analysis and/or interpretation and final manuscript approval; JMRBAE: data collection and methodology; TOV: conceptualization, methodology, and performance of surgeries and/or experiments; LDABA: data analysis and/or interpretation, methodology, and writing – review & editing; SPLXS: project management, investigation, methodology, software, and validation; LFRM: data collection and conceptualization; CRM: writing – original draft and software; and SCR: investigation and writing – review & editing.




Publikationsverlauf

Eingereicht: 21. September 2024

Angenommen: 06. Februar 2025

Artikel online veröffentlicht:
30. April 2025

© 2025. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution 4.0 International License, permitting copying and reproduction so long as the original work is given appropriate credit (https://creativecommons.org/licenses/by/4.0/)

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Bibliographical Record
Jefferson Lessa Soares de Macedo, Jovita Maria Rafael Batista de Albuquerque Espíndola, Thamara de Oliveira Vasconcelos, Luna D'Angelis Barbosa de Albuquerque, Sarah Pereira Lima Xavier da Silva, Luis Felipe Rosa de Macedo, Cecilia Rosa de Macedo, Simone Correa Rosa. Dermatofibrossarcoma protuberante no couro cabeludo: Relato de caso. Revista Brasileira de Cirurgia Plástica (RBCP) – Brazilian Journal of Plastic Surgery 2025; 40: s00451807279.
DOI: 10.1055/s-0045-1807279
 

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