Abstract
Background: The surgical management of Ebstein's anomaly represents a major challenge. Methods: Thirty consecutive patients with Ebstein's anomaly received surgical treatment in
the period from April 2002 to October 2009. Operations included annuloplasty, repair
of the tricuspid valve using autologous pericardium and tricuspid valve replacement.
In most cases, repair of the tricuspid valve was done using autologous pericardium
instead of an annuloplasty with the anterior leaflet alone. Associated congenital
malformations were also repaired during the operation. Follow-up ranged from 6 to
82 months. Results: Intraoperative transesophageal echocardiography revealed no or only minimal tricuspid
incompetence after cardiopulmonary bypass in 25 patients. Mild or moderate incompetence
was observed in 3 and 2 patients, respectively. At the last follow-up echocardiography,
5 patients with mild and 2 patients with moderate tricuspid incompetence were detected.
There was no sign of pericardial degeneration, tricuspid valve stenosis, or calcification
of the pericardial patch in any patient during follow-up. Conclusions: Although further study is required to assess the long-term function of the reconstructed
tricuspid valve, our early and midterm results from this current study indicate that
repairing the tricuspid valve with autologous pericardium achieves reasonable outcomes
in the majority of patients with Ebstein's anomaly, including pediatric and adult
patients.
Key words
ebstein's anomaly - annuloplasty - autologous pericardium
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Dr. Zhong-ya Yan
Department of Cardiac Surgery The Affiliated Provincial Hospital of Anhui Medical University Cardiovascular Disease Institute of Anhui Province
No. 17 Lujiang Road
Hefei 230001
China
Telefon: +86 0 55 12 28 34 40
Fax: +86 0 55 12 28 34 40
eMail: shajiming@163.com