Dancing Eyes Syndrome - Brainstem Acoustic Evoked Potential Approach

Abstract

Three patients with dancing eyes syndrome of childhood are reported focussing on brainstem acoustic evoked potentials (BAEPs) recorded at different phases of the disease. In the first child in the acute phase BAEPs revealed pontine disturbance, which was less severe in a following milder attack. In the second child slight BAEP abnormalities were shown in the period of remission. In the case of the third child minimal pontine abnormalities were registered by BAEPs.

These electrophysiological findings, in accordance with the clinical features, suggest tegmento-pontine or pontocerebellar localisation of pathology in the dancing eyes syndrome.

Key words

Dancing eyes syndrome - Opsoclonus-myoclonus-ataxia - Brainstem acoustic - Evoked potentials - Pons - Pontocerebellar connections