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Rofo 2022; 194(03): 310-312
DOI: 10.1055/a-1555-3762
DOI: 10.1055/a-1555-3762
The Interesting Case
Erdheim Chester Disease Mimicking Lymphoma: A Case Report
Background
Erdheim Chester disease (ECD) is a rare disorder, characterized by organ infiltration of non-Langerhans cell foamy, CD68+, CD1a- histiocytes. Since first described in 1930 by William Chester, > 900 cases have been reported. The disease usually affects patients in the 5th – 7th decade of life with a predilection for males [1] [2] [3].
Publication History
Article published online:
14 October 2021
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References
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