ABSTRACT
We describe the first report of distal obstructive uropathy and prune-belly syndrome
in an infant with amniotic band syndrome. Prenatal ultrasonographic examination in
the third trimester revealed intermittent oligohydramnios, bilateral hydronephrosis,
and megacystis. Postnatally, the infant was found to have a scalp defect, a skin pedicle,
pseudosyndactyly and constriction rings on the hands, marked distention of the abdomen,
a fibrous band attached to the proximal urethra causing urethral stricture, a swollen
penile shaft, bilateral talipes equinovarus, and syndactyly of the feet. Multiple
fibrous amniotic bands could be identified in the placenta. Our case shows that fetal
distal obstructive uropathy can be associated with the congenital constriction band
syndrome.
Keywords
Distal obstructive uropathy - prune-belly syndrome - amniotic band syndrome