Long-Term Outcome in Children with Congenital Unilateral Facial Nerve Palsy

During a 20-year period (1980 - 1999) 12 children with isolated congenital unilateral facial nerve palsy were seen at our hospital. The only child delivered by forceps made a full recovery from his palsy within two months, whereas functional improvement in patients with non-traumatic delivery was generally poor. In two patients the palsy affected predominantly the upper periocular region. In 10 children the lower facial region seemed to be mainly involved. Cognitive outcome was within normal limits, with one exception. Conventional neuroimaging was not contributory to the understanding of the pathogenetic mechanisms. We conclude that the majority of congenital unilateral facial nerve palsies are not of traumatic origin and carry a poor functional prognosis.

Key words

Congenital facial nerve palsy - Facial nerve palsy - Birth trauma - Depressor anguli oris muscle - Congenital lower lip palsy - Moebius syndrome

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