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Semin intervent Radiol 2022; 39(03): 261-270
DOI: 10.1055/s-0042-1751260
DOI: 10.1055/s-0042-1751260
Review Article
Pulmonary Arteriovenous Malformations: What the Interventional Radiologist Should Know
Abstract
Pulmonary arteriovenous malformations (PAVMs) are abnormal connections between the pulmonary artery and pulmonary vein bypassing the normal capillary bed causing a right-to-left shunt. The majority (80–90%) of PAVMs are associated with hereditary hemorrhagic telangiectasia (HHT). PAVMs may be asymptomatic or present with symptoms of hypoxia, shortness of breath, migraines, sequelae of paradoxical embolization, or rupture. Transcatheter embolization has become the standard of care. This article will review the clinical presentation, workup, genetics, imaging findings, embolization, complications, and follow-up for patients with PAVMs.
Keywords
hereditary hemorrhagic telangiectasia - pulmonary arteriovenous malformation - embolization - interventional radiologyPublication History
Article published online:
31 August 2022
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