Int J Angiol 2024; 33(03): 202-204
DOI: 10.1055/s-0041-1727136
Case Report

Cor Triatriatum Dexter with Noncompaction of Right Ventricle and Complete Heart Block: An Unholy Trinity

1   Department of Cardiology, King George's Medical University, Lucknow, Uttar Pradesh, India
,
1   Department of Cardiology, King George's Medical University, Lucknow, Uttar Pradesh, India
,
Pravesh Vishwakarma
1   Department of Cardiology, King George's Medical University, Lucknow, Uttar Pradesh, India
,
Rishi Sethi
1   Department of Cardiology, King George's Medical University, Lucknow, Uttar Pradesh, India
› Institutsangaben

Abstract

Cor triatriatum (CT) or a triatrial heart is a rare congenital anomaly in which one of the atrial chambers is divided by a fibromuscular membrane. Of the two variants, CT dexter (right-sided CT) is still further rare than CT sinister (left-sided CT). Although CT sinister presents with features of left heart obstructive disease mimicking mitral stenosis, CT dexter is usually asymptomatic and is found incidentally on imaging. Here, we present a patient with an unusual case of complete heart block who was found to have CT dexter along with right ventricular noncompaction on imaging.



Publikationsverlauf

Artikel online veröffentlicht:
30. Juli 2021

© 2021. International College of Angiology. This article is published by Thieme.

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