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J Pediatr Intensive Care 2022; 11(01): 077-082
DOI: 10.1055/s-0040-1715849
Case Report

Giant Right Atrial Myxoma with Fulminant Progression in an Infant

Ebru Azapagasi
1   Division of Pediatric Intensive Care Unit, Dr. Sami Ulus Maternity and Children’s Training and Research Hospital, Ankara, Turkey
,
Mutlu Uysal Yazici
1   Division of Pediatric Intensive Care Unit, Dr. Sami Ulus Maternity and Children’s Training and Research Hospital, Ankara, Turkey
,
Mehmet Emre Ari
2   Division of Pediatric Cardiology, Dr. Sami Ulus Maternity and Children’s Training and Research Hospital, Ankara, Turkey
,
Rabia Sedef Karakaya
3   Department of Pediatri, Keçiören Training and Research Hospital, Ankara, Turkey
,
Hasibe Gökçe Cınar
4   Department of Radiology, Dr. Sami Ulus Children’s Health and Diseases Training and Research Hospital, Ankara, Turkey
,
Mehmet Tasar
5   Department of Pediatric Cardiovascular Surgery, Dr. Sami Uĺus Chiĺdren’s Heaĺth and Diseases Training and Research Hospitaĺ, Ankara, Turkey
,
Safak Gucer
6   Departman of Pediatric Pathoĺogy, Hacettepe University Facuĺty of Medicine, Ankara, Turkey
› Author Affiliations Funding None.
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Abstract

Cardiac myxoma is rare in children. Myxomas are exceedingly rare in infancy. Right atrial myxomas were recorded in a small number of case reports involving infants worldwide. We report the case of a 2-month-old infant with giant right atrial myxoma. The case presented to our hospital with respiratory distress, and had pericardial and pleural effusion. Diagnosis of cardiac tumor was made with the aid of computerized tomography scan and echocardiogram. The tumor size was 3.1 × 3.4 × 3.9 cm. The patient worsened rapidly and had sudden cardiac arrest which did not respond to interventions. Postmortem cardiac autopsy confirmed the diagnosis of myxoma on gross examination and histology. This article aims to focus attention to the atypical size and location of this atrial myxoma, causing diagnostic difficulty in this infant.

Keywords

giant right atrial myxoma - infant - fulminant progression - sudden cardiac arrest

Consent for Publication

Written informed consent was obtained from the patient's family for his anonymized information to be published in this article.




Publication History

Received: 08 March 2020

Accepted: 02 July 2020

Article published online:
31 August 2020

© 2020. Thieme. All rights reserved.

Georg Thieme Verlag KG
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