Cognitive Ability in Children with Chronic Granulomatous Disease: A Comparison of Those Managed Conservatively with Those Who Have Undergone Hematopoietic Stem Cell Transplant

Abstract

Chronic granulomatous disease (CGD) is a primary immunodeficiency managed conservatively or with hematopoietic stem cell transplant. Studies have shown people with CGD and those transplanted for primary immunodeficiencies have lower than average cognitive ability. In this study, IQ in children with CGD and those transplanted for it was within the normal range.

Keywords

cognitive ability - chronic granulomatous disease - hematopoietic stem cell transplant

• References

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