Askin tumor is a tumor of the thoracopulmonary region that most commonly affects children
and adolescents. These rare tumors are a form of primitive neuroectodermal tumor and
typically carry a poor prognosis. Treatment is multimodal and consists of a combination
of neoadjuvant chemotherapy, radical resection, and adjuvant chemo- and radiotherapy
or all of the above. Surgery is advocated in most cases. We report a case of Askin
tumor in a 54-year-old male who showed rapid and complete response to neoadjuvant
chemotherapy. This allowed potentially radical surgery to be avoided. At one-year
follow-up he remains disease-free.
Neoadjuvant therapy - chest wall - sarcoma