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Klin Padiatr 2019; 231(01): 4-13
DOI: 10.1055/a-0669-9271
Übersicht
© Georg Thieme Verlag KG Stuttgart · New York

Die Rasch Progessive Glomerulonephritis im Kindesalter

Rapid Progressive Glomerulonephritis in Children
Ulrike Mayer
1   Pediatric Nephrology, Hannover Medical School, Hannover
,
Jan Hinrich Bräsen
2   Pathology, Hannover Medical School, Hannover
,
Lars Pape
1   Pediatric Nephrology, Hannover Medical School, Hannover
› Author Affiliations
Further Information

Publication History

Publication Date:
25 September 2018 (online)

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Zusammenfassung

Die rasch progressive Glomerulonephritis (RPGN) im Kindesalter stellt eine seltene aber schwere Erkrankung dar, die häufig zu einer dialysepflichtigen Niereninsuffizienz führt. In diesem Review wird die Definition der RPGN dargestellt und das grundsätzliche diagnostische und therapeutische Vorgehen inklusive Nierenbiopsie werden diskutiert. Darüber hinaus werden die Besonderheiten einzelner Krankheitsentitäten beschrieben, die eine RPGN verursachen können und entsprechende diagnostische und therapeutische Besonderheiten dargestellt.

Abstract

Rapid Progressive Glomerulonephritis (RPGN) is a rare but very severe disease in children that often leads to acute and/or chronic renal failure requiring dialysis therapy. In this review, diagnostic criteria of RPGN including renal biopsy are discussed. An overview on general therapeutic strategies is discussed. Entities/diseases that cause RPGN are then described and special diagnostic and therapeutic features are given.

Schlüsselwörter

Kinder - Glomerulonephritis - Akutes Nierenversagen - Dialyse

Key words

Children - Glomerulonephritis - acute kidney injury - Dialysis
 

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