ABSTRACT
Ehlers-Danlos syndrome (EDS) is a heterogeneous group of inherited connective tissue
disorders with at least ten distinct types. We report a case of EDS complicated by
cervical incompetence. Treatment was undertaken after confirmation that the patient's
EDS was not type IV, hence not associated with potentially serious vascular complications.
Because of concern about stretching or tearing of the hyperextensible connective tissue
associated with EDS, cerclage was not performed. The cervical incompetence due to
defective connective tissue was treated with a Smith-Hodge pessary.
