Symptomatic Progression of Congenital Ulnar Nerve Hypoplasia with Brachial Plexus Anomaly

Symptomatic progression of congenital ulnar nerve hypoplasia in association with an anomaly of the brachial plexus is uncommon. The authors present such a case involving an 11-year-old girl, who presented with a complaint of progressive numbness and hand weakness occurring in less than 6 months' time. Physical examination revealed limb hypoplasia, neurologic abnormalities, and a palpable hypoplastic ulnar nerve at the level of the cubital tunnel. An additional intraoperative finding was an anomalous brachial plexus. This combined case of congenital ulnar nerve hypoplasia, brachial plexus anomaly, and symptomatic progression, is discussed in the context of other literature.

KEYWORDS

Congenital ulnar nerve hypoplasia - brachial plexus anomaly - progression

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