Congenital Partial Pericardial Defect in a Neonate: A Case Report

Surasak Puvabanditsin; Eugene Garrow; Anjali Biswas; Angela Davydov; Manuel Gomez; Passara Liangthanasarn

doi:10.1055/s-2003-40011

American Journal of Perinatology, Table of Contents

Am J Perinatol 2003; 20(3): 121-124
DOI: 10.1055/s-2003-40011

Congenital Partial Pericardial Defect in a Neonate: A Case Report

Surasak Puvabanditsin¹ , Eugene Garrow² , Anjali Biswas¹ , Angela Davydov¹ , Manuel Gomez¹ , Passara Liangthanasarn¹

¹Department of Pediatrics, Jersey City Medical Center, New Jersey
²Department of Surgery, Jersey City Medical Center, New Jersey

Abstract

ABSTRACT

This report describes a neonate with congenital partial absence of the pericardium associated with hypoplastic left heart syndrome. The patient presented with severe heart failure caused by a hypoplastic left ventricle. The infant died at 15 hours of age because of intractable congestive heart failure. Necropsy revealed, in addition to a hypoplastic left ventricle, a transverse biventricular constriction suggestive of partial absence of the pericardium. In addition to cardiovascular malformations, a left hydronephrosis and a bicornuate uterus was found. We report a rare clinical entity and review the literature.

KEYWORDS

Congenital partial pericardial defect - hypoplastic left heart syndrome - neonate

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References

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