Atypischer lipomatöser Tumor des Oberschenkels mit metaplastischer Ossifikation

Zusammenfassung

Wir berichten über den Fall eines ausgedehnten atypischen lipomatösen Tumors (ALT) mit metaplastischer Ossifikation am rechten Oberschenkel eines 45-jährigen Patienten. Nach jahrelanger langsamer Progredienz wurde die Indikation zur Exzision aufgrund von Schmerzhaftigkeit und einer auffälligen Verhärtung gestellt. Sonografisch und intraoperativ ließen sich innerhalb des Tumors Verkalkungen darstellen. Histologisch zeigte sich ein ALT mit metaplastischer Ossifikation. Beim Nachweis einer verkalkten subkutanen Weichgewebs-Raumforderung sollte somit auch diese seltene Differenzialdiagnose in Betracht gezogen werden.

Abstract

We report the rare case of an atypical lipomatous tumor (ALT) of the right thigh with metaplastic ossification in a 45-year-old patient. After 17 years of slow progress the tumor was excised due to sonographic changes, growing, painfulness and palpable hardening. Sonographically and intraoperatively, calcifications could be observed within the tumor. Histologically, an ALT was found with metaplastic ossification. Therefore ALT with metaplastic ossification should be taken into consideration as a possible differential diagnosis when detecting a calcified subcutaneous soft tissue mass.

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