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DOI: 10.1055/s-0042-1749171
Retrograde Type A Aortic Dissection 48 Hours after TEVAR in a Patient with a Delayed Diagnosis of Vascular Ehlers-Danlos Syndrome
Authors
Funding None.

Abstract
We report a case of a fatal retrograde Type A aortic dissection following thoracic endovascular aortic repair (TEVAR). The patient was diagnosed with vascular Ehlers-Danlos syndrome (vEDS) only postoperatively, which is a relative contraindication for TEVAR. The patient had no major or minor criteria for vEDS. This case report emphasizes pitfalls of TEVAR in patients with a connective tissue disorder.
Keywords
acute aortic syndrome - aortic dissection - thoracic endovascular aortic repair - vascular Ehlers-Danlos syndrome - connective tissue disorderPublikationsverlauf
Eingereicht: 11. April 2021
Angenommen: 24. September 2021
Artikel online veröffentlicht:
01. November 2022
© 2022. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)
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