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DOI: 10.1055/s-0040-1722567
Infantile Isolated Absence of Right Pulmonary Artery with an Absent Stump and No Collaterals
Abstract
Unilateral absence of pulmonary artery (UAPA) is a rare entity. Diagnosis is often incidental based on echocardiography (ECHO)/computed tomography (CT) findings done for a cardiac evaluation or recurrent pulmonary pathology not responding to conventional treatment. Childhood-onset symptoms are often rare, and most of these cases are reported in adulthood or postpuberty. Here, we present a 5-month-old child with an isolated absence of right pulmonary artery without even an arterial stump or collaterals. Treatment options depend on the severity of symptoms and anatomy of the abnormal vessels, and in some cases, patients get better, if not completely well with the available medical and surgical treatments.
Keywords
unilateral absence of pulmonary artery - UAPA without collaterals - isolated absence of right pulmonary arteryPublikationsverlauf
Eingereicht: 11. Oktober 2020
Angenommen: 03. Dezember 2020
Artikel online veröffentlicht:
09. Februar 2021
© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)
Georg Thieme Verlag KG
Rüdigerstraße 14, 70469 Stuttgart, Germany
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