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CC BY-NC-ND 4.0 · Journal of Health and Allied Sciences NU 2011; 01(04): 53-54
DOI: 10.1055/s-0040-1703543
Case Report

ELLIS VAN CREVELD SYNDROME WITH PARTIAL ATRIOVENTRICULAR CANAL DEFECT, PERSISTENT LEFT SUPERIOR VENA CAVA, DUAL CORONARY SINUS OSTIAE - A CASE REPORT

Mundayat Gopalakrishnan
1   Division of Cardiovascular and Thoracic Surgery, K.S. Hegde Medical Academy, Nitte University, Mangalore - 575 018, Karnataka, India
,
Manjunath Kamath
2   Division of Cardiac Anaesthesiology, K.S. Hegde Medical Academy, Nitte University, Mangalore 575018, Karnataka, India
,
Krishna Prasad Patla
2   Division of Cardiac Anaesthesiology, K.S. Hegde Medical Academy, Nitte University, Mangalore 575018, Karnataka, India
,
Kodangala Subramanyam
3   Division of Cardiology, K.S. Hegde Medical Academy, Nitte University, Mangalore 575018, Karnataka, India
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Abstract

Ellis van Creveld syndrome (EVCS) is a congenital defect with skeletal and cardiac anomalies. We have operated on a 30 year old female with EVCS having single atrium, severe mitral and tricuspid regurgitation, bilateral superior venacavae, double coronary sinus ostiae .Anterior Mitral cleft repair, a tricuspid annuloplasty, rerouting of left superior venacava and septal patching were done. She made a smooth recovery

Keywords

congenital heart disease - partial AV canal defect


Publication History

Article published online:
04 May 2020

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