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Am J Perinatol 2019; 36(S 02): S22-S28
DOI: 10.1055/s-0039-1691773
Review Article
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Updates in Congenital Heart Disease: Can Outcomes Improve?

Gerard R. Martin
1   Division of Cardiology, Children's National Heart Institute, George Washington University School of Medicine, Washington, District of Columbia
,
Russell R. Cross
1   Division of Cardiology, Children's National Heart Institute, George Washington University School of Medicine, Washington, District of Columbia
,
Lisa A. Hom
1   Division of Cardiology, Children's National Heart Institute, George Washington University School of Medicine, Washington, District of Columbia
,
Darren Klugman
1   Division of Cardiology, Children's National Heart Institute, George Washington University School of Medicine, Washington, District of Columbia
2   Division of Cardiac Critical Care Medicine, Children's National Heart Institute, George Washington University School of Medicine, Washington, District of Columbia
› Author Affiliations
Further Information

Publication History

Publication Date:
25 June 2019 (online)

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Abstract

Despite numerous advances in medical and surgical management, congenital heart disease (CHD) remains the number one cause of death in the first year of life from congenital malformations. The current strategies used to approach improving outcomes in CHD are varied. This article will discuss the recent impact of pulse oximetry screening for critical CHD, describe the contributions of advanced cardiac imaging in the neonate with CHD, and highlight the growing importance of quality improvement and safety programs in the cardiac intensive care unit.

Keywords

congenital heart disease - quality improvement - pulse oximetry screening
 

  • References

  • 1 Hoffman JI, Kaplan S. The incidence of congenital heart disease. J Am Coll Cardiol 2002; 39 (12) 1890-1900
    CrossrefPubMedGoogle Scholar
  • 2 Raissadati A, Nieminen H, Haukka J, Sairanen H, Jokinen E. Late causes of death after pediatric cardiac surgery: a 60-year population-based study. J Am Coll Cardiol 2016; 68 (05) 487-498
    CrossrefPubMedGoogle Scholar
  • 3 Petrini J, Damus K, Damus R. Trends in Infant Mortality Attributable to Birth Defects–United States, 1980–1995. Morbidity and Mortality Weekly Report (MMWR). Available at: https://www.cdc.gov/mmwr/preview/mmwrhtml/00054921.htm . Accessed May 14, 2019
    PubMedGoogle Scholar
  • 4 Mahle WT, Newburger JW, Matherne GP. , et al; American Heart Association Congenital Heart Defects Committee of the Council on Cardiovascular Disease in the Young, Council on Cardiovascular Nursing, and Interdisciplinary Council on Quality of Care and Outcomes Research; American Academy of Pediatrics Section on Cardiology And Cardiac Surgery; Committee On Fetus And Newborn. Role of pulse oximetry in examining newborns for congenital heart disease: a scientific statement from the AHA and AAP. Pediatrics 2009; 124 (02) 823-836
    CrossrefPubMedGoogle Scholar
  • 5 Oster ME, Lee KA, Honein MA, Riehle-Colarusso T, Shin M, Correa A. Temporal trends in survival among infants with critical congenital heart defects. Pediatrics 2013; 131 (05) e1502-e1508
    CrossrefPubMedGoogle Scholar
  • 6 Eckersley L, Sadler L, Parry E, Finucane K, Gentles TL. Timing of diagnosis affects mortality in critical congenital heart disease. Arch Dis Child 2016; 101 (06) 516-520
    CrossrefPubMedGoogle Scholar
  • 7 Gardiner HM, Kovacevic A, van der Heijden LB. , et al. Prenatal screening for major congenital heart disease: assessing performance by combining national cardiac audit with maternity data. Heart 2014; 100 (05) 375-382
    CrossrefPubMedGoogle Scholar
  • 8 Plana MN, Zamora J, Suresh G, Fernandez-Pineda L, Thangaratinam S, Ewer AK. Pulse oximetry screening for critical congenital heart defects. Cochrane Database Syst Rev 2018; 3: CD011912
    PubMedGoogle Scholar
  • 9 Glidewell J, Grosse SD, Riehle-Colarusso T. , et al. Actions in support of newborn screening for critical congenital heart disease - United States, 2011-2018. MMWR Morb Mortal Wkly Rep 2019; 68 (05) 107-111
    CrossrefPubMedGoogle Scholar
  • 10 Abouk R, Grosse SD, Ailes EC, Oster ME. Association of US state implementation of newborn screening policies for critical congenital heart disease with early infant cardiac deaths. JAMA 2017; 318 (21) 2111-2118
    CrossrefPubMedGoogle Scholar
  • 11 Kellenberger CJ, Yoo S-J, Büchel ER. Cardiovascular MR imaging in neonates and infants with congenital heart disease. Radiographics 2007; 27 (01) 5-18
    CrossrefPubMedGoogle Scholar
  • 12 Tsai-Goodman B, Geva T, Odegard KC, Sena LM, Powell AJ. Clinical role, accuracy, and technical aspects of cardiovascular magnetic resonance imaging in infants. Am J Cardiol 2004; 94 (01) 69-74
    CrossrefPubMedGoogle Scholar
  • 13 Puranik R, Muthurangu V, Celermajer DS, Taylor AM. Congenital heart disease and multi-modality imaging. Heart Lung Circ 2010; 19 (03) 133-144
    CrossrefPubMedGoogle Scholar
  • 14 Fratz S, Chung T, Greil GF. , et al. Guidelines and protocols for cardiovascular magnetic resonance in children and adults with congenital heart disease: SCMR expert consensus group on congenital heart disease. J Cardiovasc Magn Reson 2013; 15: 51
    CrossrefPubMedGoogle Scholar
  • 15 Taylor AJ, Cerqueira M, Hodgson JM. , et al; American College of Cardiology Foundation Appropriate Use Criteria Task Force; Society of Cardiovascular Computed Tomography; American College of Radiology; American Heart Association; American Society of Echocardiography; American Society of Nuclear Cardiology; North American Society for Cardiovascular Imaging; Society for Cardiovascular Angiography and Interventions; Society for Cardiovascular Magnetic Resonance. ACCF/SCCT/ACR/AHA/ASE/ASNC/NASCI/SCAI/SCMR 2010 Appropriate Use Criteria for Cardiac Computed Tomography. A Report of the American College of Cardiology Foundation Appropriate Use Criteria Task Force, the Society of Cardiovascular Computed Tomography, the American College of Radiology, the American Heart Association, the American Society of Echocardiography, the American Society of Nuclear Cardiology, the North American Society for Cardiovascular Imaging, the Society for Cardiovascular Angiography and Interventions, and the Society for Cardiovascular Magnetic Resonance. J Cardiovasc Comput Tomogr 2010; 4 (06) 407.e1-407.e33
    PubMedGoogle Scholar
  • 16 Valsangiacomo Buechel ER, Grosse-Wortmann L, Fratz S. , et al; EACVI. Indications for cardiovascular magnetic resonance in children with congenital and acquired heart disease: an expert consensus paper of the Imaging Working Group of the AEPC and the Cardiovascular Magnetic Resonance Section of the EACVI. Eur Heart J Cardiovasc Imaging 2015; 16 (03) 281-297
    CrossrefPubMedGoogle Scholar
  • 17 Sarikouch S, Schaeffler R, Körperich H, Dongas A, Haas NA, Beerbaum P. Cardiovascular magnetic resonance imaging for intensive care infants: safe and effective?. Pediatr Cardiol 2009; 30 (02) 146-152
    CrossrefPubMedGoogle Scholar
  • 18 Windram J, Grosse-Wortmann L, Shariat M, Greer M-L, Crawford MW, Yoo S-J. Cardiovascular MRI without sedation or general anesthesia using a feed-and-sleep technique in neonates and infants. Pediatr Radiol 2012; 42 (02) 183-187
    CrossrefPubMedGoogle Scholar
  • 19 Gaies M, Cooper DS, Tabbutt S. , et al. Collaborative quality improvement in the cardiac intensive care unit: development of the Paediatric Cardiac Critical Care Consortium (PC4). Cardiol Young 2015; 25 (05) 951-957
    CrossrefPubMedGoogle Scholar
  • 20 Anderson JB, Brown DW, Lihn S. , et al. Power of a learning network in congenital heart disease. World J Pediatr Congenit Heart Surg 2019; 10 (01) 66-71
    CrossrefPubMedGoogle Scholar
  • 21 Brunetti MA, Gaynor JW, Retzloff LB. , et al. Characteristics, risk factors, and outcomes of extracorporeal membrane oxygenation use in pediatric cardiac ICUs: a report from the Pediatric Cardiac Critical Care Consortium Registry. Pediatr Crit Care Med 2018; 19 (06) 544-552
    CrossrefPubMedGoogle Scholar
  • 22 Clauss SB, Anderson JB, Lannon C. , et al. Quality improvement through collaboration: the National Pediatric Quality Improvement Collaborative initiative. Curr Opin Pediatr 2015; 27 (05) 555-562
    CrossrefPubMedGoogle Scholar
  • 23 Alten JA, Klugman D, Raymond TT. , et al. Epidemiology and outcomes of cardiac arrest in pediatric cardiac ICUs. Pediatr Crit Care Med 2017; 18 (10) 935-943
    CrossrefPubMedGoogle Scholar
  • 24 Riley CM, Merritt AD, Mize JM, Schuette JJ, Berger JT. Assuring sustainable gains in interdisciplinary performance improvement: creating a shared mental model during operating room to cardiac ICU handoff. Pediatr Crit Care Med 2017; 18 (09) 863-868
    CrossrefPubMedGoogle Scholar
  • 25 Gaies M, Anderson J, Kipps A. , et al; Cardiac Networks United Executive Committee and Advisory Board. Cardiac Networks United: an integrated paediatric and congenital cardiovascular research and improvement network. Cardiol Young 2018; ;(December): 1-8
    PubMedGoogle Scholar