Abstract
Rosai–Dorfman disease (RDD) is an uncommon benign histiocytic proliferative disorder
commonly involving the cervical lymph nodes and, less frequently, extranodal sites.
The histological hallmark of RDD is emperipolesis displayed by lesional histiocytes.
Central nervous system involvement is rare and usually intracranial; intramedullary
spinal involvement is even less common and, to our knowledge, rarely reported in children.
Herein, we report a case of RDD with isolated intramedullary spinal involvement in
a child, which, to our knowledge, is the first case reported in an infant.
Keywords
Rosai-Dorfman disease - histiocytic disorder - intramedullary spinal cord masses
