Am J Perinatol 2016; 33(05): 425-432
DOI: 10.1055/s-0035-1565996
Review Article
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Persistent Urogenital Sinus: Diagnostic Imaging for Clinical Management. What Does the Radiologist Need to Know?

Anna Lia Valentini
1   Department of Radiological Sciences, Institute of Radiology, Catholic University of Sacred Heart, Rome, Italy
,
Michela Giuliani
1   Department of Radiological Sciences, Institute of Radiology, Catholic University of Sacred Heart, Rome, Italy
,
Benedetta Gui
1   Department of Radiological Sciences, Institute of Radiology, Catholic University of Sacred Heart, Rome, Italy
,
Maria Elena Laino
1   Department of Radiological Sciences, Institute of Radiology, Catholic University of Sacred Heart, Rome, Italy
,
Viola Zecchi
1   Department of Radiological Sciences, Institute of Radiology, Catholic University of Sacred Heart, Rome, Italy
,
Elena Rodolfino
1   Department of Radiological Sciences, Institute of Radiology, Catholic University of Sacred Heart, Rome, Italy
,
Valeria Ninivaggi
1   Department of Radiological Sciences, Institute of Radiology, Catholic University of Sacred Heart, Rome, Italy
,
Carlo Manzoni
2   Department of Surgical Sciences, Institute of Pediatric Radiology, University of Sacred Heart, Rome, Italy
,
Lorenzo Bonomo
1   Department of Radiological Sciences, Institute of Radiology, Catholic University of Sacred Heart, Rome, Italy
› Author Affiliations
Further Information

Publication History

29 July 2015

02 September 2015

Publication Date:
21 October 2015 (online)

Abstract

Background Persistent urogenital sinus (PUGS) is a congenital pathological condition characterized by an abnormal communication between the urethra and vagina. It may be a part of a complex syndrome and can be more often associated with congenital malformations affecting the genitourinary tract system (33%) such as intersex, rectovaginal communication, bladder agenesis, absence of vagina, and hydrocolpos. The correct radiological assessment of PUGS is especially useful for clinicians since the exact anatomical evaluation of this abnormality is a crucial factor for surgical planning. The imaging study modalities, which are essentially based on ultrasonography, voiding cystourethrography, and magnetic resonance imaging, could be misinterpreted if not correctly performed.

Aim The aim of this article is to highlight this rare pathological condition and to help general radiologists in achieving the correct technical approach for the diagnosis. Special attention will be paid in discussing the role of different imaging modalities and their contribution to the diagnosis and clinical management of patients.

 
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