Thorac Cardiovasc Surg 2012; 60(06): 428-430
DOI: 10.1055/s-0030-1271017
Case Reports
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Erdheim-Chester Disease in a Female Cardiac Surgery Patient

H. R. Mahoozi
1  Clinic for Thoracic and Cardiovascular Surgery, Heart Center NRW, Bad Oeynhausen, Germany
,
A. Zittermann
1  Clinic for Thoracic and Cardiovascular Surgery, Heart Center NRW, Bad Oeynhausen, Germany
,
K. Hakim Meibodi
1  Clinic for Thoracic and Cardiovascular Surgery, Heart Center NRW, Bad Oeynhausen, Germany
,
W. Burchert
2  Institute of Radiology, Nuclear Medicine and Molecular Imaging, Bad Oeynhausen, Germany
,
J. F. Gummert
1  Clinic for Thoracic and Cardiovascular Surgery, Heart Center NRW, Bad Oeynhausen, Germany
,
N. Mirow
1  Clinic for Thoracic and Cardiovascular Surgery, Heart Center NRW, Bad Oeynhausen, Germany
› Author Affiliations
Further Information

Publication History

10 February 2011
21 February 2011

08 March 2011

Publication Date:
18 May 2011 (online)

Abstract

We report a case of Erdheim-Chester disease (ECD) with isolated cardiac involvement in a 74-year-old female patient. The patient initially presented with superior vena cava syndrome and PET-CT imaging demonstrating an obstructing hypermetabolic lesion in the right atrium, and a distinct nonobstructing hypermetabolic lesion in the left atrium, expected to be malignant. There was no evidence of extracardiac disease. At surgical exploration, consistent with malignancy, the right atrial tumor was found to have grown into the pericardium and was resected to address symptoms and for histological diagnosis which revealed ECD on immunohistochemistry. We conclude that isolated cardiac ECD should be included in the surgical strategy for cardiac tumors showing infiltrative growth.