ABSTRACT
The aim of this study was to examine prenatal diagnosis of double-outlet right ventricle
(DORV)-associated anomalies and prognosis of each case. Medical records were reviewed
of fetuses with DORV who had fetal echocardiography at our institution from 2002 to
2006. Pre- and postnatal diagnosis and outcome were compared and evaluated. Twenty-one
fetuses were diagnosed with DORV. The pregnancy was terminated in seven cases. Three
cases had chromosomal abnormalities; three cases, hypoplastic left ventricle; and
one case, encephalocele. Accurate prenatal diagnosis of the ventricular septal defect,
outflow obstruction, and great artery relationship was achieved in 14 of 16 cases
(87.5%). Only 2 of 13 live-born cases survived beyond 6 months. The overall prognosis
for fetuses with DORV is poor. DORV is found in fetuses with a huge spectrum of associated
cardiac and extracardiac anomalies. Careful assessment by fetal echocardiography can
determine important anatomic details with adequate correctness for precise counseling.
KEYWORDS
Fetal echocardiography - double-outlet right ventricle - prenatal diagnosis - prognosis
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Ali GedikbasiM.D.
Atakoy 11, Kisim, Lale Apt. D.40
34710 Istanbul, Turkey
eMail: alged_1971@yahoo.com
