Posteriores kortikales Atrophie-Plus-Syndrom. Eine Kasuistik

Zusammenfassung

Die posteriore kortikale Atrophie (PCA) ist eine seltene neurodegenerative Erkrankung, die mit komplexen Sehstörungen einhergeht. Sie kann isoliert („PCA-pure“) oder zusammen mit anderen neurodegenerativen Störungen („PCA-plus“) auftreten. Die Diagnosestellung erfolgt meistens verzögert, da die Erkrankung wenig bekannt ist und oftmals initial eine ophthalmologische Ursache vermutet wird.

Abstract

Posterior cortical atrophy (PCA) is a rare neurodegenerative disease, which manifests with complex visual disturbances. PCA can present in isolation (‘PCA-pure’) or in association with other neurodegenerative disorders (‘PCA-plus’). Diagnosis is nevertheless frequently delayed, as PCA is a less known disease entity and initially a primary ocular disease is taken into consideration.

Schlüsselwörter

Benson-Syndrom - Posteriore kortikale Atrophie - Sehstörungen

Key words

Benson Syndrome - Posterior cortical Atrophy - Visual disturbances

Publication History

Received: 11 September 2019

Accepted: 18 March 2020

Article published online:
07 July 2020

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