CC BY-NC-ND 4.0 · Rev Bras Ortop (Sao Paulo) 2020; 55(01): 125-129
DOI: 10.1016/j.rbo.2018.02.006
Relato de Caso
Sociedade Brasileira de Ortopedia e Traumatologia. Published by Thieme Revinter Publicações Ltda Rio de Janeiro, Brazil

Intraosseous Neurothekeoma of the Hand in a 16-year-old Boy[*]

Article in several languages: português | English
1  Serviço de Ortopedia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Hospital Pediátrico, Coimbra, Portugal
,
Inês Maria Spencer Balacó
1  Serviço de Ortopedia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Hospital Pediátrico, Coimbra, Portugal
,
Cristina Marta da Gama Gomes Alves
1  Serviço de Ortopedia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Hospital Pediátrico, Coimbra, Portugal
,
António Gabriel de Almeida Matos
1  Serviço de Ortopedia Pediátrica, Centro Hospitalar e Universitário de Coimbra, Hospital Pediátrico, Coimbra, Portugal
› Author Affiliations
Further Information

Publication History

07 January 2018

27 February 2018

Publication Date:
19 December 2019 (online)

Abstract

Soft-tissue tumors are rare in the pediatric population. First described in 1969 as myxoma of the nerve sheath, the neurothekeoma is a benign tumor lesion with presumable origin in the nerve sheath. It occurs mainly in female children and presents as a mass of slow, subcutaneous growth, asymptomatic and without alteration of the local pigmentation. It is predominantly located in the head, neck, and extremities of the upper limbs. This report presents the case of a 16-year-old male with a tumor mass originating from the nerve sheath in the 4th left metacarpal, intraosseous, and relapsed after previous surgical resection 2 years before this observation. A marginal resection of the tumor mass was performed on the distal region of the fourth metacarpal, followed by curettage of the proximal phalanx and filling with structural autologous bone graft. The patient maintained a favorable postoperative clinical evolution, without local pain or range of motion limitation in his fingers. Radiologically, a progressive trabecular filling of the proximal phalanx of the fourth metacarpal was observed. At 17 months of follow-up, the patient is asymptomatic and shows no signs of relapse. The description of this case serves to increase the familiarity with this rare pathology, and aid its diagnosis and treatment.

* Study developed at Pediatric Orthopedics Service, Pediatric Hospital, Hospital and University Center of Coimbra, Portugal. Originally Published by Elsevier Editora Ltda.