The mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episode syndrome-associated human mitochondrial tRNALeu(UUR) mutation causes aminoacylation deficiency and concomitant reduced association of mRNA with ribosomes - Chomyn,A.; Enriquez,J.A.; Micol,V.; Fernandez-Silva,P.; Attardi,G. (J Biol Chem, 2000)