TY - JOUR AU - Zani-Ruttenstock, Elke; Zani, Augusto; Honjo, Osami; Chiu, Priscilla TI - Pentalogy of Cantrell: Is Echocardiography Sufficient in the Neonatal Period? SN - 2194-7619 SN - 2194-7627 PY - 2017 JO - European J Pediatr Surg Rep. JF - European Journal of Pediatric Surgery Reports LA - EN VL - 05 IS - 01 SP - e9 EP - e11 DA - 2017/03/22 KW - omphalocele KW - pentalogy of Cantrell KW - ectopia cordis KW - cardiac MRI AB - Pentalogy of Cantrell is a rare syndrome that is characterized by varying degrees of midline wall defects and congenital cardiac anomalies. A left ventricular diverticulum (LVD) is defined as partial ectopia cordis, can be part of the pentalogy of Cantrell, and can put the patient at risk of severe complications. Early diagnosis and ligation/resection of the LVD is important to prevent complications. We report on a case of pentalogy of Cantrell, in which a LVD was diagnosed only at 2 months of age despite preceding pre- and postnatal echocardiography. We conclude that in the suspicion of pentalogy of Cantrell, either complete or incomplete, cardiac magnetic resonance imaging should be performed, when possible, to avoid the potential complication of a herniating ventricular diverticulum. PB - Georg Thieme Verlag KG DO - 10.1055/s-0037-1599794 UR - http://www.thieme-connect.com/products/ejournals/abstract/10.1055/s-0037-1599794 ER -