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Z Orthop Unfall 1987; 125(1): 99-105
DOI: 10.1055/s-2008-1039686
© 1987 F. Enke Verlag Stuttgart

Eine neue Sonderform der Enchondromatose

A New Variant of EnchondromatosisH. Weickert, B. Friedel
  • Klinik für Orthopädie der Medizinischen Akademie Magdeburg (Direktor: OMR Prof. Dr. sc. med. H. Weickert)
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Publication Date:
18 March 2008 (online)

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Zusammenfassung

Beobachtung einer besonderen Verlaufsform der Enchondromatose. Beginn der Enchondrome in den Patellae, später stark expansives metaepiphysäres Wachstum an den Kniegelenken und distal medial an der rechten Tibia. Kälteabhängiges Exanthem, Pigmentflecke, Trommelschlegelfinger, Uhrglasnägel, Störungen der Dentition. Radikale Operation am rechten Femur brachte über 8 Jahre Beobachtung kein Rezidiv.

Abstract

A case of enchondromatosis with an unusual course was observed. The enchondromas originated in the patellae, subsequently with rapidly spreading metaepiphyseal growth on the knee joints and distally on the medial side of the right tibia. Cold-sensitive exanthema, pigment spots, drumstick fingers, watchglass nails, dentition disorders. Since radical surgery on the right femur 8 years ago there has been no recurrence.

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