Am J Perinatol 2006; 23(3): 173-176
DOI: 10.1055/s-2006-934094
Copyright © 2006 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA.

Congenital Cerebellar Primitive Neuroectodermal Tumor in a Newborn

Yavuz Köksal1 , Ali Varan1 , Nejat Akalan2 , Ahmet Bostanci3 , Aysenur Cila4 , Figen Söylemezoglu5 , Münevver Büyükpamukçu1
  • 1Department of Pediatric Oncology, Hacettepe University, Institute of Oncology, Ankara, Turkey
  • 2Department of Neurosurgery, Hacettepe University, Faculty of Medicine, Ankara, Turkey
  • 3Department of Obstetrics and Gynecology, Ankara Training and Research Hospital, Ankara, Turkey
  • 4Department of Radiology, Hacettepe University, Faculty of Medicine, Ankara, Turkey
  • 5Department of Pathology, Hacettepe University, Faculty of Medicine, Ankara, Turkey
Further Information

Publication History

Publication Date:
29 March 2006 (online)

ABSTRACT

Neonatal primitive neuroectodermal tumor is a rare clinical entity. The initial presentation in affected newborns is often subtle, nonspecific, and rarely includes neurological signs. Here we report a newborn with congenital cerebellar primitive neuroectodermal tumor. We had detected hydrocephalus and enlarged biparietal diameter at the 36th week of gestational age by fetal ultrasonography.

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Yavuz KöksalM.D. 

Fellow in Pediatric Oncology, Department of Pediatric Oncology, Hacettepe University

Institute of Oncology, 06100 Ankara, Turkey

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