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Am J Perinatol 2003; 20(3): 121-124
DOI: 10.1055/s-2003-40011
Copyright © 2003 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA. Tel.: +1(212) 584-4662

Congenital Partial Pericardial Defect in a Neonate: A Case Report

Surasak Puvabanditsin1 , Eugene Garrow2 , Anjali Biswas1 , Angela Davydov1 , Manuel Gomez1 , Passara Liangthanasarn1
  • 1Department of Pediatrics, Jersey City Medical Center, New Jersey
  • 2Department of Surgery, Jersey City Medical Center, New Jersey
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Publication History

Publication Date:
12 June 2003 (online)

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ABSTRACT

This report describes a neonate with congenital partial absence of the pericardium associated with hypoplastic left heart syndrome. The patient presented with severe heart failure caused by a hypoplastic left ventricle. The infant died at 15 hours of age because of intractable congestive heart failure. Necropsy revealed, in addition to a hypoplastic left ventricle, a transverse biventricular constriction suggestive of partial absence of the pericardium. In addition to cardiovascular malformations, a left hydronephrosis and a bicornuate uterus was found. We report a rare clinical entity and review the literature.

KEYWORDS

Congenital partial pericardial defect - hypoplastic left heart syndrome - neonate

REFERENCES

  • 1 Mcllhenny J, Campbell S E, Raible R J, Antaki G M. Congenital absence of the pericardium.  AJR Am J Roentgenol . 1996;  167 274-275
    PubMedGoogle Scholar
  • 2 Miller S W. Imaging pericardial disease.  Radiol Clin North Am . 1989;  27 1113-1125
    PubMedGoogle Scholar
  • 3 Jones J W, McManus B M. Fatal cardiac strangulation by congenital partial pericardial defect.  Am Heart J . 1984;  107 183-185
    CrossrefPubMedGoogle Scholar
  • 4 Silverman F N, Kuhn J P. Caffey's Pediatric X-ray Diagnosis: An Integrated Imaging Approach. St. Louis: Mosby 1993: 854-856
    Google Scholar
  • 5 Gassner I, Judmaier W, Fink C. et al . Diagnosis of congenital pericardial defects, including a pathognomonic sign for dangerous apical ventricular herniation, on magnetic resonance imaging.  Br Heart J . 1995;  74 60-66
    PubMedGoogle Scholar
  • 6 Grainger R G. Diagnostic Radiology New York: Longman 1986: 677-678
  • 7 Gatzoulis M A, Munk M D, Merchant N, Van Arsdell S G, McCrindle B W, Webb G D. Isolated congenital absence of the pericardium: clinical presentation, diagonsis, and management.  Ann Thorac Surg . 2000;  69 1209-1215
    CrossrefPubMedGoogle Scholar
  • 8 Connelly H M, Click R L, Schattenberg T T, Seward J B, Tajik A J. Congenital absence of the pericardium: echocardiography as diagnostic tool.  J Am Soc Echocardiogr . 1995;  8 87-92
    PubMedGoogle Scholar
  • 9 Fosburg R G, Jakubiak J V, Delany T B. Congenital partial absence of pericardium.  Ann Thorac Surg . 1968;  5 171-177
    PubMedGoogle Scholar
  • 10 Chapman J E, Rubin J W, Gross C M, Janssen M E. Congenital absence of pericardium: an unusual cause of atypical angina.  Ann Thorac Surg . 1986;  45 91-93
    PubMedGoogle Scholar
  • 11 Gehlman H R, van Ingen J G. Symptomatic congenital complete absence of the left pericardium-case report and review of the literature.  Eur Heart J . 1989;  10 670-675
    PubMedGoogle Scholar
      >