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Journal of Pediatric Neurology 2018; 16(01): 021-024
DOI: 10.1055/s-0037-1603998
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Recurrent Drop Attacks as Presenting Manifestation of Subacute Sclerosing Panencephalitis: An Atypical Presentation

Rajesh Verma
1   Department of Neurology, King George's Medical University, Lucknow, Uttar Pradesh, India
,
Aniruddha More
1   Department of Neurology, King George's Medical University, Lucknow, Uttar Pradesh, India
› Author Affiliations Funding None.
Further Information

Publication History

20 February 2017

22 May 2017

Publication Date:
20 July 2017 (online)

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Abstract

Subacute sclerosing panencephalitis (SSPE) is a potentially fatal progressive complication of measles virus infection of the brain occurring in children and adolescents. It typically presents with a progressive decline in cognitive abilities along with periodic myoclonic jerks. We report a case of SSPE with atypical presentation. Our patient presented with intermittent drop attacks without any obvious myoclonic jerks or cognitive decline making his diagnosis difficult. Atypical manifestations of SSPE occur in 10% of patients, and a high index of suspicion is necessary for early diagnosis and management of this dreaded disease.

Keywords

subacute sclerosing panencephalitis - measles virus - drop attacks - cognitive abilities - myoclonic jerks - periodic burst

Note

Written informed consent was taken from the patient/parents/legal guardians/next of kin for reporting this case.


 

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