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Semin Hear 2011; 32(4): 308-320
DOI: 10.1055/s-0031-1291935
© Thieme Medical Publishers

Audiological Management of Cogan's Syndrome

Katherine H. Teece1 , 2 , Amy P. Olund1 , 2
  • 1Department of Otorhinolaryngology, Mayo Clinic, Rochester, Minnesota
  • 2Division of Audiology, Mayo Clinic, Rochester, Minnesota
Further Information

Publication History

Publication Date:
24 October 2011 (online)

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ABSTRACT

Cogan's syndrome (CS) is a rare immune-mediated disorder resulting in sensorineural hearing loss, ocular symptoms, and other systemic symptoms. This article prepares the audiologist to evaluate and treat the hearing loss seen in patients with CS. Previously published research in the medical literature is reviewed. Results of a retrospective chart review are presented along with four representative case studies. These serve to illustrate the variability of audiometric configurations and treatment options, which include corticosteroids, hearing aids, and cochlear implants. Audiologists play a pivotal role in the patient's medical team, which may include neuro-otologists, ophthalmologists, internists, rheumatologists, and other professionals as needed. It is especially important for audiologists to recognize the signs of CS and make prompt recommendations for medical intervention.

KEYWORDS

Cogan's syndrome - hearing loss - cochlear implant - hearing aid

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Katherine H TeeceAu.D. 

Division of Audiology, Department of Otorhinolaryngology

Mayo Clinic, 200 First Street SW, Gonda 12-400, Rochester, MN 55905

Email: teece.katherine@mayo.edu

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