Therapieoptionen bei adenoidzystischem Tränendrüsenkarzinom – Fallserie und aktueller Literaturüberblick

Zusammenfassung

Das adenoidzystische Karzinom der Tränendrüse (ACC) stellt einen seltenen malignen orbitalen Tumor mit insgesamt schlechter Prognose dar. Derzeitige Therapieansätze mit radikaler und lokaler Chirurgie, adjuvanter Bestrahlung und neoadjuvanter intraarterieller Chemotherapie werden kontrovers diskutiert. Wir präsentieren 3 Fälle von Patienten mit ACC mit unterschiedlichen Therapiekonzepten und diskutieren diese mit aktuellen Empfehlungen aus der Literatur.

Abstract

Adenoid cystic carcinoma of the lacrimal gland (ACC) is a rare malignant orbital tumour with a poor overall prognosis. Current therapeutic approaches like radical and local surgery, adjuvant radiation and neoadjuvant intra-arterial chemotherapy are controversial. We present three cases of patients with ACC with different therapy concepts and discuss these with current recommendations from the literature.

Schlüsselwörter

adenoidzystisches Karzinom - Orbita - Tränendrüsentumor

Key words

adenoid cystic carcinoma - lacrimal gland tumour - orbit

• Literatur

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