DOI: 10.1055/s-00000041

Neuropediatrics

Issue 04 · Volume 28 · August 1997 DOI: 10.1055/s-002-5734

Original articles

191
Schmitt, B.; Bauersfeld, U.; Fanconi, S.; Wohlrab, G.; Huisman, T. A. G. M.; Bandtlow, Ch.; Baumann, P.; Superti-Furga, A.; Martin, E.; Arbenz, U.; Molinari, L.; Turina, M.; Boltshauser, E.; Schmid, E. R.: The Effect of the N-methyl-D-aspartate Receptor Antagonist Dextromethorphan on Perioperative Brain Injury in Children Undergoing Cardiac Surgery with Cardiopulmonary Bypass: Results of a Pilot Study
198
Gropman, A. L.; Barkovich, A. J.; Vezina, L. G.; Conry, J. A.; Dubovsky, E. C.; Packer, R. J.: Pediatric Congenital Bilateral Perisylvian Syndrome: Clinical and MRI Features in 12 Patients
204
Steinlin, M.; Schmid, M.; Landau, K.; Boltshauser, E.: Follow-Up in Children with Joubert Syndrome
212
Topaloǧlu, H.; Dinçer, P.; Richard, I.; Akçören, Z.; Alehan, D.; Özme, Ş; Çaǧlar, M.; Karaduman, A.; Urtizberea, J. A.; Beckmann, J. S.: Calpain-3 Deficiency Causes a Mild Muscular Dystrophy in Childhood
217
Sewry, C. A.; D'Alessandro, M.; Wilson, L. A.; Sorokin, L. M.; Naom, I.; Bruno, S.; Ferlini, A.; Dubowitz, V.; Muntoni, F.: Expression of Laminin Chains in Skin in Merosin-Deficient Congenital Muscular Dystrophy
223
Vainzof, M.; Costa, C. S.; Marie, S. K.; Moreira, E. S.; Reed, U.; Passos-Bueno, M. R.; Beggs, A. H.; Zatz, M.: Deficiency of α-Actinin-3 (ACTN3) Occurs in Different Forms of Muscular Dystrophy
229
Sperl, W.; Felber, S.; Skladal, D.; Wermuth, B.: Metabolic Stroke in Carbamyl Phosphate Synthetase Deficiency

Short communication

Letter to the editor

239
Weglage, J.; Bick, U.; Schuierer, G.; Pietsch, M.; Sprinz, A.; Zaß, R.; Ullrich, K.: Progression of Cerebral White Matter Abnormalities in Early Treated Patients with Phenylketonuria During Adolescence