Paget-Schroetter Syndrome

Summary

Paget-Schroetter Syndrome is a primary, effort vein thrombosis of the axillo-subclavian level. It occurs predominantly after repetitive sport movements in the dominant limb in young healthy male individuals. Patients refer with pain, swelling and blue discolouration in the affected upper extremity.

We present a 33-years-old woman with primary thrombosis of left subclavian vein, with no history of repetitive sport exercises or trauma. The patient’s profession requiring leaning against the desk for hours daily could be a trigger factor for vein thrombosis in presented case. Doppler ultrasonography and venography showed complete occlusion of left subclavian vein. Computed tomography showed no evidence for compression at thoracic outlet level. Patient was successfully treated with anticoagulants and followed for 21 months with repeated duplex ultrasound examinations. The symptoms had resolved. Long time left subclavian vein patency and good quality of life have been achieved.

Zusammenfassung

Das Paget-von-Schrötter-Syndrom ist eine primäre Thrombose des Axillo-subclavia-Bereiches. Es tritt meist nach sportlichen Wiederholungsbewegungen auf bei jungen, gesunden Männern. Patienten berichten von Schmerz, Schwellungen und blauer Verfärbung in der betroffenen oberen Extremität. Wir stellen eine 33-jährige Patientin vor mit einer primären Thrombose der linken V. subclavia ohne vergangene wiederholte sportliche Betätigung oder Trauma. Beruflich muss die Patientin täglich stundenlang gegen ein Pult lehnen, was Auslöser für die Venennthrombose sein könnte. In der Dopplersonographie und Venographie zeigte sich eine komplette Okklusion der linken V. subclavia. Die Computertomographie zeigte keine Notwendigkeit für eine Kompression bei diesem Thrombosegrad. Die Patientin wurde erfolg-reich mit Antikoagulanzien behandelt und in den nächsten 21 Monaten wiederholt mittels Duplexsonographie überwacht. Die Symptome waren nicht mehr vorhanden.

Keywords

Paget-Schroetter Syndrome - primary thrombosis - effort thrombosis - axillary vein - subclavian vein

Schlüsselwörter

Paget-von-Schroetter-Syndrom - primäre Thrombose - akute Achselvenensperre - V. axillaris - V. subclavia

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