Kongenitaler Hyperinsulinismus

Sebastian Kummer; Thomas Meissner

doi:10.1055/s-0043-108251

Pädiatrie up2date, Table of Contents

Pädiatrie up2date 2017; 12(02): 163-181
DOI: 10.1055/s-0043-108251

Endokrinologie/Stoffwechsel

Georg Thieme Verlag KG Stuttgart · New York

Kongenitaler Hyperinsulinismus

Sebastian Kummer

,

Thomas Meissner

Abstract

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Der kongenitale Hyperinsulinismus ist die häufigste Ursache für eine persistierende Hypoglykämie-Neigung im frühen Kindesalter. Dieser Beitrag gibt einen praxisorientierten Überblick über Ursachen, Diagnosestellung und Therapie dieser Erkrankung.

Schlüsselwörter

hypoketotische Hypoglykämie - Hyperinsulinismus - Glukagon - Somatostatin - ABCC8 - KCNJ11

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References

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