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DOI: 10.1055/s-0038-1640302
Sarcoidosis of the Temporal Bone
Introduction:
Sarcoidosis a chronic, idiopathic, multisystemic disease of unknown etiology with frequent pulmonary and lymphatic systemic manifestations (90%). Manifestations in the head and neck are occuring in 10% of the patients with Sarcoidosis.
Methods:
case report: A 40 year old male adult is presenting a progressive hearing loss since a couple of years as well as a mild pressure felling over the mastoid. Two years before he had surgery of the right nasolacrimal duct.
Results:
The clinical examination of the tympanic membran and the ear by microscope was regulary and without any pathology. Audiometrically we see a sensoneurial hearing loss of 1 KHz by 40 dB up to 4 KHz by 60 dB. MR shows a chronic mastoititis as well as a meningitis. The labyrinth was without any pathology. In the OR mastoidectomy was performed. Frozen section showed a granulomatous inflammation. After fixation the diagnosis of the sarcoidosis were proposed.
Conclusions:
This is a rare case of a extrapulmonary sarcoidosis in the mastoid. A CT of the thorax showed a sarcoidosis stage I with bihilare lymphatic manifestation. The patient responded to the treatment with Soludecortin of 50 mg/d. The hearing loss is still persisting.
No conflict of interest has been declared by the author(s).
Publication History
Publication Date:
18 April 2018 (online)
© 2018. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).
Georg Thieme Verlag KG
Stuttgart · New York