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Klinische Neurophysiologie 2014; 45(04): 230-232
DOI: 10.1055/s-0034-1387348
DOI: 10.1055/s-0034-1387348
Der besondere Fall
Zwerchfellstimulation bei Amyotropher Lateralsklerose mit respiratorischem Onset
Diaphragm Pacing in Amyotrophic Lateral Sclerosis with Respiratory OnsetFurther Information
Publication History
Publication Date:
07 October 2014 (online)
Dem Fallbericht liegt eine ungewöhnliche Erstmanifestation der Amyotrophen Lateralsklerose (ALS) mit Atembeschwerden zugrunde, wobei die Notwendigkeit einer nichtinvasiven Heimbeatmung (NIV) bereits vor Diagnosestellung bestand. Aufgrund der besonderen Befundkonstellation wurde bei erhaltener Leitfähigkeit des N. phrenicus ein Zwerchfellschrittmacher implantiert. Diese Therapieoption wurde in Deutschland bei ALS bisher nur in Einzelfällen angewendet.
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Literatur
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