Rosette-Forming Glioneuronal Tumor of the Fourth Ventricle

Introduction

Komori et al. (2002) were the first authors to recognize the existence of a new brain tumor entity, rosette-forming glioneuronal tumor (RGNT) of the fourth ventricle. The authors described 11 cases of this distinctive tumor of the posterior fossa [6]. A few further RGNT cases were published in the following 5 years [1] [2] [4] [5] [8] [10], eventually leading to the inclusion of RGNT in the 4^th edition of the WHO brain tumor classification as a benign primary brain tumor classified as WHO grade 1 [7] [9].

We describe here the clinical and neuroradiological features of a further patient with RGNT of the fourth ventricle. Our report may contribute to establishing the natural history of these tumors and identifying the best course of treatment.

References

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