Nasal paraganglioma: A case report and literature review

Summary

Introduction: Paragangliomas are neuroendocrine tumors that most commonly originate in the adrenal gland, a type that is called pheochromocytoma; however, 5–10% of paragangliomas are extra-adrenal and may arise in any area between the neck and pelvic region along the sympathetic nervous system. Those located in the head and neck comprise 3% of extra-adrenal tumors, with the majority originating in the tympanic–jugular region and carotid body.

Objective: To present a rare case of nasal paraganglioma and review the literature.

Case report: The patient was submitted to medial subtotal maxillectomy, and her clinical findings, diagnostic data, and treatment outcome were recorded.

Conclusion: Paragangliomas are considered benign tumors, but they occasionally display a malignant character. The most important finding in this case was the need for total resection of the tumor to avoid recurrence.

Keywords

Paraganglioma - Neuroendocrine Tumors - Nasal Cavity - Adrenal Gland Neoplasms - Neoplasms

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