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Int Arch Otorhinolaryngol 2012; 16(03): 406-409
DOI: 10.7162/S1809-97772012000300018
Case Report
Thieme Publicações Ltda Rio de Janeiro, Brazil

Cochlear implantation in patient with Dandy-walker syndrome

Adriana Kosma Pires de Oliveira
1   Otolaryngological Doctor at Hospital of Parana of Otolaryngology.
,
Rogerio Hamerschmidt
2   Professor of Otolaryngology, Federal University of Parana. Otolaryngologist Doctor at, Hospital of Parana of Otolaryngology.
,
Marcos Mocelin
3   Head of the Department of Otolaryngology, Clinics Hospital, Federal University of Parana. Head of the Department of Otolaryngology, Clinics Hospital, Federal University of Parana.
,
Rodrigo K. Rezende
4   Resident of Otolaryngology at the Clinics Hospital, Federal University of Parana.
› Author Affiliations
Further Information

Publication History

02 June 2010

01 August 2010

Publication Date:
05 December 2013 (online)

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Summary

Introduction: Dandy Walker Syndrome is a congenital abnormality in the central nervous system, characterized by a deficiency in the development of middle cerebelar structures, cystic dilatation of the posterior pit communicating with the fourth ventricle and upward shift of the transverse sinuses, tentorium and dyes. Among the clinical signs are occipital protuberances, a progressive increase of the skull, bowing before the fontanels, papilledema, ataxia, gait disturbances, nystagmus, and intellectual impairment.

Objectives: To describe a case of female patient, 13 years old with a diagnosis of this syndrome and bilateral hearing loss underwent cochlear implant surgery under local anesthesia and sedation.

Case Report: CGS, 13 years old female was referred to the Otolaryngological Department of Otolaryngology Institute of Parana with a diagnosis of “Dandy-Walker syndrome” for Otolaryngological evaluation for bilateral hearing loss with no response to the use of hearing aids.

Final Comments: The field of cochlear implants is growing rapidly. We believe that the presence of Dandy-Walker syndrome cannot be considered a contraindication to the performance of cochlear implant surgery, and there were no surgical complications due to neurological disorders with very favorable results for the patient who exhibits excellent discrimination. It has less need for lip reading with improvement in speech quality.

Keywords

hearing loss - cochlear implants - Dandy-Walker syndrome
 

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