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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2019; 29(04): 452-456
DOI: 10.4103/ijri.IJRI_463_18
Case Report

Prenatally diagnosed case of tricuspid valve dysplasia: A case report with review of the literature

Prateek Agarwal
Department of Radiodiagnosis, Kempegowda Institute of Medical Sciences, Bengaluru, Karnataka
,
Rajesh Agarwal
Department of Ultrasound, Meera Hospital, Shiv Marg, Bani Park, Jaipur, Rajasthan, India
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

We present a case of fetal tricuspid valve dysplasia (TVD) and pulmonary atresia, diagnosed during a routine obstetric ultrasound scan. Serial fetal echocardiographic evaluations revealed progressively augmented prodigious thickening of the tricuspid valvular and subvalvular structures, which eventually extensively obliterated the right ventricle cavity. Thickened dysplastic valve displayed a “cotton-wool” appearance. Unusual configurations of three vessels in the three-vessel view were also observed on a consecutive gray scale and color Doppler scans. During pregnancy, the fetus exhibited satisfactory growth parameters, and complications of progressive hemodynamic compromise associated with TVD and pulmonary atresia such as grievous hydrops or arrhythmia did not develop till 39 weeks of gravidity.

Keywords

Dysplasia - non-immune hydrops - pulmonary atresia - tricuspid annulus - tricuspid regurgitation - tricuspid valve


Publication History

Received: 06 December 2018

Accepted: 23 October 2019

Article published online:
21 July 2021

© 2019. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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