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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2020; 30(01): 77-80
DOI: 10.4103/ijri.IJRI_277_19
Case Report

MDCT evaluation of intramyocardialsinusoids-coronary artery communications in a neonate with pulmonary atresia and intact ventricular septum

Karuna M Das
Department of Radiology, College of Medicine and Health Sciences, Al Ain, UAE
,
Taleb M Almansoori
Department of Paediatric Cardiology, Prince Salman Heart Center, King Fahad Medical City, Riyadh, Saudi Arabia
,
Tarek Suliman Momenah
Department of Radiology, College of Medicine and Health Sciences, Al Ain, UAE
,
Klaus Neidl-Van Gorkom
Department of Radiology, College of Medicine and Health Sciences, Al Ain, UAE
› Author Affiliations Financial support and sponsorship Nil.
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Abstract

A patient of tetrology of Fallot with complete atresia of the pulmonary outflow tract with ventriculocoronary connections is presented.MDCT imaging revealed left coronary sinus, with a large fistula draining into the free wall of hypoplastic right ventricular cavity with tortuous channel arising from right ventricular outflow, and communicating with proximal limb of the fistula forming a complete loop suggesting a right ventricle–to – left coronary sinus sinusoid.

Keywords

Intramyocardial sinusoids - multidetector computed tomography - pulmonary atresia


Publication History

Received: 26 June 2019

Accepted: 23 November 2019

Article published online:
19 July 2021

© 2020. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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  • References

  • 1 Freedom RM, Harrington DP. Contributions of intramyocardial sinusoids in pulmonary atresia and intact ventricular septum to a right-sided circular shunt. Br Heart J 1974; 36: 1061-5
    CrossrefPubMedGoogle Scholar
  • 2 Lenox CC, Briner J. Absent proximal coronary arteries associated with pulmonic atresia. Am J Cardiol 1972; 30: 666-9
    CrossrefPubMedGoogle Scholar
  • 3 Giglia TM, Mandell VS, Connor AR, Mayer JE, Lock JE. Diagnosis and management of right ventricle-dependent coronary circulation in pulmonary atresia with intact ventricular septum. Circulation 1992; 86: 1516-28
    CrossrefPubMedGoogle Scholar
  • 4 Dusek J, Ostádal B, Duskova M. Postnatal persistence of spongy myocardium with embryonic blood supply. Arch Pathol 1975; 99: 312-7
    PubMedGoogle Scholar
  • 5 Luo L, Kebede S, Wu S, Stouffer GA. Coronary artery fistulae. Am J Med Sci 2006; 332: 79-84
    CrossrefPubMedGoogle Scholar
  • 6 Tiryakioglu SK, Gocer H, Tiryakioglu O, Kumbay E. Multiple coronary-cameral fistulae. Tex Heart Inst J 2010; 37: 378-9
    PubMedGoogle Scholar
  • 7 Yamanaka O, Hobbs RE. Coronary artery anomalies in 126,595 patients undergoing coronary arteriography. Cathet Cardiovasc Diagn 1990; 21: 28-40
    CrossrefPubMedGoogle Scholar
  • 8 Stierle U, Giannitsis E, Sheikhzadeh A, Potratz J. Myocardial ischemia in generalized coronary artery-left ventricular microfistulae. Int J Cardiol 1998; 63: 47-52
    CrossrefPubMedGoogle Scholar
  • 9 Heidenreich FP, Leon DF, Shaver JA. A case of anomalous right coronary artery to right atrial fistula presenting as atypical aortic insufficiency. Am J Cardiol 1969; 23: 453-7
    CrossrefPubMedGoogle Scholar
  • 10 Schanzenbächer P, Bauersachs J. Acquired right coronary artery fistula draining to the right ventricle: Angiographic documentation of first appearance following reperfusion after acute myocardial infarction, with subsequent spontaneous closure. Heart 2003; 89: e22
    CrossrefPubMedGoogle Scholar
  • 11 Schumacher G, Roithmaier A, Lorenz HP, Meisner H, Sauer U, Müller KD. et al. Congenital coronary artery fistula in infancy and childhood: Diagnostic and therapeutic aspects. Thorac Cardiovasc Surg 1997; 45: 287-94
    Article in Thieme ConnectPubMedGoogle Scholar
  • 12 Zheng J, Gao B, Zhu Z, Shi G, Xu Z, Liu J. et al. Surgical results for pulmonary atresia with intact ventricular septum: A single-centre 15-year experience and medium-term follow-up. Eur J Cardiothorac Surg 2016; 50: 1083-8
    CrossrefPubMedGoogle Scholar